Hearing Impairment, Deafness

DISABILITY CATEGORY

Hearing Impairments, including Deafness

TYPES

DEFINITION(S)

Our nation’s special education law, the Individuals with Disabilities Education Act (IDEA) defines deafness as...

“a hearing impairment so severe that a child is impaired in processing linguistic information through hearing, with or without amplification, that adversely affects a child's educational performance.”

[34 Code of Federal Regulations §300.8(c) (3)]

Our nation’s special education law, the Individuals with Disabilities Education Act (IDEA) defines hearing impairment as...

“an impairment in hearing, whether permanent or fluctuating, that adversely affects a child's educational performance but that is not included under the definition of deafness.”

[34 Code of Federal Regulations §300.8(c) (5)]

Other definitions

Hearing loss is generally described as slight, mild, moderate, severe or profound, depending upon how well a person can hear the intensities or frequencies most strongly associated with speech. Impairments in hearing can occur in both areas (loudness and/or frequency), and may exist in only one ear or in both ears. Generally, only children whose hearing loss is greater than 90 decibels are considered deaf. (NICHCY, 2010)

FACTS AND STATS

Each year in the United States, more than 12,000 babies are born with a hearing loss; often, the cause is unknown. Profound deafness occurs in 4-11 per 10,000 children; in at least 50% of these cases, the cause is genetic. (NICHCY, 2010)

CAUSES

Hearing loss can be either acquired, meaning the loss occurred after birth due to illness or injury; or congenital, meaning that the hearing loss or deafness was present at birth. The most common cause of acquired hearing loss is exposure to noise. Other causes can include: build up of fluid behind the eardrum; ear infections; childhood diseases, such as mumps, measles, or chicken pox; and head trauma. Congenital causes of hearing loss and deafness include: a family history of hearing loss or deafness; infections during pregnancy (such as rubella); and complications during pregnancy (such as the Rh factor, maternal diabetes, or toxicity). A child's hearing loss or deafness may also be characteristic of another disability of Down syndrome, Usher syndrome, Treacher Collins syndrome, Crouzon syndrome, and Alport syndrome. (NICHCY, 2010)

Conductive hearing losses are caused by diseases or obstructions in the outer or middle ear. Conductive hearing losses usually affect all frequencies of hearing evenly and do not result in severe losses. A person with conductive hearing loss is usually able to use a hearing aid well or can be helped medically or surgically.

Sensorineural hearing losses result from damage to the delicate sensory hair cells of the inner ear of the nerves that supply it. These hearing losses can range from mild to profound.They often affect the person's ability to hear certain frequencies more than others. Thus, even with amplification to increase the sound level, a person with sensorineural hearing loss may perceive distorted sounds, sometimes making the successful use of a hearing aid impossible. 

A mixed hearing loss refers to a combination of conductive and sensorineural loss.

A central hearing loss can results from damage or impairment to the nerves or nuclei of the central nervous system, either in the pathways to the brain or in the brain itself. (ASHA, 2012)

PREVENTION

The National Organization for Hearing Research Foundation provides suggestions in preventing hearing loss. Loud noise is the leading cause of preventable hearing loss and the use of ear plugs and ear protection can help prevent injury. Regular medical examinations and proper immunizations can help prevent diseases and infections that may lead to hearing loss. With proper preventive measures, factors that contribute to permanent hearing loss can be detected early and remedied.

CHARACTERISTICS

If you observe any of the following behaviors or symptoms of hearing loss, you should consider having your child's hearing evaluated further by a certified audiologist.

MEDICAL TREATMENT

The treatment of hearing loss depends on the cause. A bacterial infection of the middle ear can be treated with antibiotics; blockages of the outer and middle ears can be cleared; damaged eardrums can be repaired surgically; and ossicles affected by otosclerosis can be replaced with artificial bones. Some causes of sensorineural hearing loss can also be improved. For example, an acoustic neuroma can be removed surgically.

If there is no cure for the hearing loss (as with age-related hearing loss), a hearing aid for one or both ears usually helps most people, whether the hearing loss is the result of conductive or sensorineural problems. Many different types of hearing aids are available and the audiologist will advise as to which type best suits your needs.

Cochlear implants can be particularly valuable for deaf children when they are implanted around the age of two or three, the time when language skills are developing fastest.

Audiologic rehabilitation is also available to help train to improve hearing. Hearing rehabilition focuses on adjusting to hearing loss, making the best use of hearing aids, exploring assistive devices, managing conversations, and taking charge of communication. (ASHA, 2012)

PROGNOSIS

Children who are hard of hearing will find it much more difficult than children who have normal hearing to learn vocabulary, grammar, word order, idiomatic expressions, and other aspects of verbal communication. For children who are deaf or have severe hearing losses, early, consistent, and conscious use of visible communication modes (such as sign language, finger spelling, and Cued Speech) and/or amplification and aural/oral training can help reduce this language delay. By age four or five, most children who are deaf are enrolled in school on a full-day basis and do special work on communication and language development. (NICHCY, 2010)

EDUCATIONAL IMPLICATIONS

Hearing loss or deafness does not affect a person's intellectual capacity or ability to learn. However, children who are either hard of hearing or deaf generally require some form of special education services in order to receive an adequate education. Such services may include:

ORGANIZATIONS

Alexander Graham Bell Association for the Deaf and Hard of Hearing

3417 Volta Place NW 
Washington, DC 20007
202-337-5220 202-337-5221 (TTY)
www.agbell.org

The Alexander Graham Bell Association for the Deaf and Hard of Hearing (AG Bell) is a lifelong resource, support network and advocate for listening, learning, talking and living independently with hearing loss. Through publications, advocacy, training, scholarships and financial aid, AG Bell promotes the use of spoken language and hearing technology. Headquartered in Washington, D.C., with chapters located in the United States and a network of international affiliates, AG Bell's global presence provides its members and the public with the support they need – close to home. With over a century of service, AG Bell supports its mission: Advocating Independence through Listening and Talking!

American Sign Language Teachers Association

P.O. Box 92445 
Rochester, New York 14692-9998
www.aslta.org

The American Sign Language Teachers Association - ASLTA is the only national organization dedicated to the improvement and expansion of the teaching of ASL and Deaf Studies at all levels of instruction. ASLTA is an individual membership organization of more than 1,000 ASL and Deaf Studies educators from elementary through graduate education as well as agencies.

American Society for Deaf Children (ASDC)

3820 Hartzdale Drive
Camp Hill, PA 17011
1-800-942-2732; 717-703-0073 1-866-895-4206 (TTY)
www.deafchildren.org

The American Society for Deaf Children supports and educates families of deaf and hard of hearing children and advocates for high quality programs and services. ASDC was founded in 1967 as a parent-helping-parent organization. Today, ASDC is a national, independent non-profit organization whose purpose is providing support, encouragement, and information to families raising children who are deaf or hard of hearing.

American Speech-Language Hearing Association

10801 Rockville Pike
Rockville, Maryland 20852
1-800-638-8255
www.asha.org

ASHA is the professional, scientific, and credentialing association for more than 123,000 members and affiliates who are audiologists, speech-language pathologists, and speech, language, and hearing scientists.

Gaullaudet University Laurent Clerc National Deaf Education Center

800 Florida Ave. NE
Washington, DC 20002
clerccenter.gallaudet.edu/

Gaullaudet University’s Laurent Clerc National Deaf Education Center shares the concerns of parents and professionals about the achievement of deaf and hard of hearing students in different learning environments across the country. We all know that deaf and hard of hearing students can and do excel, but we also know that not all deaf and hard of hearing students are achieving their full potential.

National Association of the Deaf 

8630 Fenton Street
Suite 820
Silver Spring, MD 20910-3819
301-587-1788 301-587-1789 (TTY)
www.nad.org

The National Association of the Deaf (NAD), established in 1880, is the oldest and largest constituency organization safeguarding the accessibility and civil rights of 28 million deaf and hard of hearing Americans in education, employment, health care, and telecommunications. A private, non-profit organization, the NAD is a dynamic federation of 51 state association affiliates including the District of Columbia, organizational affiliates, and direct members.

RESOURCES

Web sites